Neonatal correction of ectopia cordis and onphalocele: successful case report
نویسندگان
چکیده
Female neonate diagnosed with ectopia cordis and omphalocele was submitted to an operation at 6 hours of age to reconstruct the abdominal wall and place the heart in the left pleural space. After initial hemodynamic instability the patient was reoperated to open the sternum; with progressive recovery, extubation occurred on the 15th postoperative day and she was discharged on the 40th day. With 8 months of life a new operation was successfully performed to close the sternum and reconstruct the abdominal wall. After 4 years, the child is asymptomatic with no necessity of medications or physical restrictions. Descriptors: Heart defects, congenital, surgery. Abdominal wall, abnormalities, surgery. Abnormalities, multiple, surgery. Resumo Recém-nascido, sexo feminino, com diagnóstico de ectopia cordis e onfalocele; realizada cesariana e com 6 horas correção da parede abdominal e da ectopia cordis. Evoluiu com grave instabilidade hemodinâmica, sendo reoperada para liberação dos pontos do esterno. Apresentou melhora progressiva, extubação no 15o e alta no 40o dia. Aos oito meses foi reinternada para fechamento do esterno e reconstrução abdominal (neoonfaloplastia). Houve boa evolução, com alta no 5o dia. Com 4 anos de evolução, encontra-se assintomática, sem medicações ou restrições físicas. Descritores: Cardiopatias congênitas, cirurgia. Parede abdominal, anormalidades, cirurgia. Anormalidades múltiplas, cirurgia. Correção de ectopia cordis e onfalocele em recém-nascido: relato de caso operado com sucesso Neonatal correction of ectopia cordis and onphalocele: successful case report
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